The Diagnosis and Treatment of Pulmonary Arterial Hypertension Due to Rare Causes_Chinese Journal of Respiratory and Critical Care Medicine

Authors：

 GAO Yuanming , ZHANG Xiangfeng , LIU Shuang

Department of Respiratory Medicine, Beijing Anzhen Hospital Affiliated to Capital Medical University. Beijing, 100029, China;

Corresponding author：

GAO Yuanming, Email: gao_yuanming@yahoo.com.cn

Keywords：

Pulmonary arterial hypertension; Etiology; Primary biliary cirrhosis; Hyperthyroidism; Antiphospholipid syndrome; Pulmonary artery sarcoma

Video：

Export PDF Favorites Scan Get Citation

Abstract Full text Figures/Tables Video References Cited by

Objective To investigate the diagnosis and treatment of pulmonary arterial hypertension ( PAH) due to rare causes. Methods The clinical presentation, laboratory testing, diagnosis and treatment of 4 patients with PAH associated with rare causes in Beijing Anzhen Hospital from January 2001 to March 2008 were analysed retrospectively. Results Primary biliary cirrhosis, hyperthyroidism, antiphospholipid syndrome and pulmonary artery sarcoma may cause PAH, which were improved after corresponding diagnosis and management. Conclusion PAH can result from rare causes. The enhancement of its recognition will help earlier diagnosis and treatment and improve the prognosis.

Citation： GAO Yuanming,ZHANG Xiangfeng,LIU Shuang. The Diagnosis and Treatment of Pulmonary Arterial Hypertension Due to Rare Causes. Chinese Journal of Respiratory and Critical Care Medicine, 2009, 09(1): 68-71. doi: Copy

1.	黄燕, 李为民. 结缔组织病与肺动脉高压研究进展. 中国呼吸与危重监护杂志, 2007, 6: 473-475.
2.	Mantz FA, Craig E. Portal axis thrombosis with spontaneous portacaval shunt and resultant cor pulmonale. Arch Pathol Lab Med, 1951 ,52: 91-97.
3.	Yohida EM, Erb SR, Ostrow DN, et al. Pulmonary hypertension associated with primary biliary cirrhosis in the absence of portal hypertension:a case report. Gut, 1994, 35: 280-282.
4.	沈敏, 张桓, 张奉春. 原发性胆汁性肝硬化合并肺动脉高压的临床分析. 中华医学杂志, 2005, 85: 946-948.
5.	Nakchbandi IA, Wirth JA, Inzucchi SE. Pulmonary hypertension caused by Graves’thyrotoxicosis: normal pulmonary hemodynamics restored by 131I treatment. Chest, 1999, 116: 1483-1485.
6.	Benjaminov FS, Prentice M, Sniderman KW, et al. Portpulmonanry hypertension in decompensated cirrhosis with refractory ascites. Gut,2003, 52: 1355-1362.
7.	Budhiraja R, Hassoun PM. Portpulmonary hypertension: a tale of two circulation. Chest, 2003, 123: 562-572.
8.	Ronald C. Thyrotoxicosis as a risk factor for pulmonary arterial hypertension. Ann Intern Med, 2006, 144: 222.
9.	吴红花, 郭晓燕, 高燕明. 甲状腺功能亢进性心脏病75 例临床分析. 中华医学杂志, 2007, 87: 262-264.
10.	Marvisi M, Brianti M, Marani G, et al. Hyperthyroidismand pulmonary hypertension. Respir Med, 2002, 96: 215-220.
11.	Yazar A, Doven O, Atis S, et al. Systolic pulmonary artery pressure and serum uric acid levels in patients with hyperthyroidism. Arch Med Res, 2003, 34: 35-40.
12.	单渊东, 曾学军, 黄晓明, 主编. 内科疑难病诊断— 协和医生临床思维例释. 北京: 中国协和医科大学出版社, 2007, 265-271.
13.	熊长明, 程显声, 柳志红, 等. 肺动脉肉瘤误诊为肺血栓栓塞症三例原因分析. 中华结核和呼吸杂志, 2004, 27: 737-739.
14.	Kim JH, Gutierrez FR, Lee EY, et al. Primary leiomyosarcoma of the pulmonary artery: a diagnostic dilemma. Clin Imaging,2003,27: 206-211.
15.	Parish JM, Rosenow ES, Swensen SJ, et al. Pulmonary artery sarcoma:clinical features. Chest, 1996, 110: 1480-1488.

1. 黄燕, 李为民. 结缔组织病与肺动脉高压研究进展. 中国呼吸与危重监护杂志, 2007, 6: 473-475.
2. Mantz FA, Craig E. Portal axis thrombosis with spontaneous portacaval shunt and resultant cor pulmonale. Arch Pathol Lab Med, 1951 ,52: 91-97.
3. Yohida EM, Erb SR, Ostrow DN, et al. Pulmonary hypertension associated with primary biliary cirrhosis in the absence of portal hypertension:a case report. Gut, 1994, 35: 280-282.
4. 沈敏, 张桓, 张奉春. 原发性胆汁性肝硬化合并肺动脉高压的临床分析. 中华医学杂志, 2005, 85: 946-948.
5. Nakchbandi IA, Wirth JA, Inzucchi SE. Pulmonary hypertension caused by Graves’thyrotoxicosis: normal pulmonary hemodynamics restored by 131I treatment. Chest, 1999, 116: 1483-1485.
6. Benjaminov FS, Prentice M, Sniderman KW, et al. Portpulmonanry hypertension in decompensated cirrhosis with refractory ascites. Gut,2003, 52: 1355-1362.
7. Budhiraja R, Hassoun PM. Portpulmonary hypertension: a tale of two circulation. Chest, 2003, 123: 562-572.
8. Ronald C. Thyrotoxicosis as a risk factor for pulmonary arterial hypertension. Ann Intern Med, 2006, 144: 222.
9. 吴红花, 郭晓燕, 高燕明. 甲状腺功能亢进性心脏病75 例临床分析. 中华医学杂志, 2007, 87: 262-264.
10. Marvisi M, Brianti M, Marani G, et al. Hyperthyroidismand pulmonary hypertension. Respir Med, 2002, 96: 215-220.
11. Yazar A, Doven O, Atis S, et al. Systolic pulmonary artery pressure and serum uric acid levels in patients with hyperthyroidism. Arch Med Res, 2003, 34: 35-40.
12. 单渊东, 曾学军, 黄晓明, 主编. 内科疑难病诊断— 协和医生临床思维例释. 北京: 中国协和医科大学出版社, 2007, 265-271.
13. 熊长明, 程显声, 柳志红, 等. 肺动脉肉瘤误诊为肺血栓栓塞症三例原因分析. 中华结核和呼吸杂志, 2004, 27: 737-739.
14. Kim JH, Gutierrez FR, Lee EY, et al. Primary leiomyosarcoma of the pulmonary artery: a diagnostic dilemma. Clin Imaging,2003,27: 206-211.
15. Parish JM, Rosenow ES, Swensen SJ, et al. Pulmonary artery sarcoma:clinical features. Chest, 1996, 110: 1480-1488.

Chinese Journal of Respiratory and Critical Care Medicine

The Diagnosis and Treatment of Pulmonary Arterial Hypertension Due to Rare Causes

Abstract Full text Figures/Tables Video References Cited by

Previous Article

Next Article

Format

Content