韧带样型纤维瘤病的诊治进展_West China Medical Journal

Authors：

陈雪莲 ,  岑瑛

Corresponding author：

岑瑛, Email: chenxl.1.27@qq.com

Keywords：

韧带样型纤维瘤病; 临床特点; 诊治; 手术; 综述

DOI：

10.7507/1002-0179.20130478

Video：

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韧带样型纤维瘤病是具有向病灶周围局部组织和（或）器官侵袭性生长、但无转移性潜力特性的一类肿瘤性疾病，组织学分类包括肌纤维母细胞性肿瘤、成纤维细胞性肿瘤和两者混合型肿瘤。该病发病率较低，且相对散在，因其临床表现及该病的检验方法和影像学检查不具有明显特征性，目前诊断多依据术后病理检查结果。这不仅局限了临床上对此病的研究，同时也加大了临床诊治的难度。很多研究报道所含患者例数少，其结论尚无定论，甚至出现互相矛盾的结果。现就其近期诊治等方面的进展进行综述。

Citation： 陈雪莲,岑瑛. 韧带样型纤维瘤病的诊治进展. West China Medical Journal, 2013, 28(10): 1512-1515. doi: 10.7507/1002-0179.20130478 Copy

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2.	Schiessling S, Kihm M, Ganschow P,et al. Desmoid tumour biology in patients with familial adenomatous polyposis coli[J]. Br J Surg, 2013, 100(5): 694-703.
3.	Micke O, Seegenschmiedt MH. Radiation therapy for aggressivefibromatosis (desmoids tumors): results of anationnalpatterns of care study[J]. Int J Radiat Oncol Biol Phys, 2005, 61(3): 882-891.
4.	Mignemi NA, Itani DM, Fasig JH, et al. Signal transduction pathway analysis in desmoid-type fibromatosis: transforming growth factor-β, COX2 and sex steroid receptors[J]. Cancer Sci, 2012, 103(12): 2173-2180.
5.	任燕燕.纤维瘤病诊治进展[J]. 浙江中医药大学学报, 2010, 34(1): 127-128.
6.	周杭城,王志华,吴海波.韧带样型纤维瘤病21例临床病理分析[J].安徽卫生职业技术学院学报, 2009, 8(5): 15-16.
7.	蔡健华,赵任. Gardner综合征早期诊断和治疗新进展[J].外科理论与实践, 2010, 15(2): 201-203.
8.	王德玲, 李卉, 谢传淼, 等. 韧带样纤维瘤的影像学表现及病理特点[J]. 中国医学影像技术, 2012, 28(1): 148-151.
9.	张红英, 柯琦, 张璋, 等. 连接素-β和雌激素受体在韧带样型纤维瘤病中的表达[J].四川大学学报·医学版, 2010, 41(1): 101-105.
10.	Vandevenne JE,De SchepperAM,De BeuckeleerL, et al. Newconcepts in understanding evolution of desmoid tumors: MR imaging of 30 lesions[J]. EurRadio, 1997, 7(7): 1013-1019.
11.	赵晶, 戴景蕊, 鲁北. 腹部纤维瘤病的CT表现及临床特点[J].临床放射学杂志, 2010, 29(12): 1633-1636.
12.	李然, 张伟国, 王毅.胸部韧带样纤维瘤的影像学分析(附4例报告及文献复习)[J]. 现代肿瘤医学, 2010, 18(8): 1554-1557.
13.	Hood B, Benglis DM, Levi AD, et al. Occiput to thoracic fusion after surgical resection of desmoids tumor[J]. World Neurosurg, 2013, 79(1): 207. e15-207. e18.
14.	Lucas DR, al-Abbadi M, Tabaczka P, et al. c-Kit expression in desmoids fibromatosis. Comparative immunohistochemical evaluation of two commercial antibodies[J]. Am J Clin Pathol, 2003, 119(3): 339-345.
15.	黄恺,傅红. 韧带样瘤的诊治进展及热点问题[J]. 中国癌症杂志, 2010, 20(3): 227-231.
16.	黄恺, 王春萌, 师英强, 等. 151例韧带样瘤的疗效及预后分析[J].中国癌症杂志, 2011, 21(1): 61-66.
17.	Gronchi A, Casali PG, Mariani L, et al. Quality of surgery and outcome in extra-abdominal aggressive fibromatosis: a series of patients surgically treated at a single institution[J]. J Clin Oncol, 2003, 21(7): 1390-1397.
18.	Bonvalot S, Eldweny H, Haddad V, et al. Extra-abdominal primary fibromatosis: aggressive management could be avoided in a subgroup of patients [J]. EJSO, 2008, 34(4): 462-468.
19.	陈懿,马洪良.手术联合放疗治疗腹壁外侵袭性纤维瘤病[J].中国现代医学杂志, 2009, 4(19): 631.

1. 　Goidblum J, Fletcher JA．Desmoid-type fibromatosis[M]//Fletche CD, Unni KK, Mertens F. World Health Organization classification of tumors：pathology and genetics of tumors of soft tissue and bone. Lyon: IARC Press, 2002: 83-84．.
2. 　Schiessling S, Kihm M, Ganschow P,et al. Desmoid tumour biology in patients with familial adenomatous polyposis coli[J]. Br J Surg, 2013, 100(5): 694-703.
3. 　Micke O, Seegenschmiedt MH. Radiation therapy for aggressivefibromatosis (desmoids tumors): results of anationnalpatterns of care study[J]. Int J Radiat Oncol Biol Phys, 2005, 61(3): 882-891.
4. 　Mignemi NA, Itani DM, Fasig JH, et al. Signal transduction pathway analysis in desmoid-type fibromatosis: transforming growth factor-β, COX2 and sex steroid receptors[J]. Cancer Sci, 2012, 103(12): 2173-2180.
5. 　任燕燕.纤维瘤病诊治进展[J]. 浙江中医药大学学报, 2010, 34(1): 127-128.
6. 　周杭城,王志华,吴海波.韧带样型纤维瘤病21例临床病理分析[J].安徽卫生职业技术学院学报, 2009, 8(5): 15-16.
7. 　蔡健华,赵任. Gardner综合征早期诊断和治疗新进展[J].外科理论与实践, 2010, 15(2): 201-203.
8. 　王德玲, 李卉, 谢传淼, 等. 韧带样纤维瘤的影像学表现及病理特点[J]. 中国医学影像技术, 2012, 28(1): 148-151.
9. 　张红英, 柯琦, 张璋, 等. 连接素-β和雌激素受体在韧带样型纤维瘤病中的表达[J].四川大学学报·医学版, 2010, 41(1): 101-105.
10. 　Vandevenne JE,De SchepperAM,De BeuckeleerL, et al. Newconcepts in understanding evolution of desmoid tumors: MR imaging of 30 lesions[J]. EurRadio, 1997, 7(7): 1013-1019.
11. 　赵晶, 戴景蕊, 鲁北. 腹部纤维瘤病的CT表现及临床特点[J].临床放射学杂志, 2010, 29(12): 1633-1636.
12. 　李然, 张伟国, 王毅.胸部韧带样纤维瘤的影像学分析(附4例报告及文献复习)[J]. 现代肿瘤医学, 2010, 18(8): 1554-1557.
13. 　Hood B, Benglis DM, Levi AD, et al. Occiput to thoracic fusion after surgical resection of desmoids tumor[J]. World Neurosurg, 2013, 79(1): 207. e15-207. e18.
14. 　Lucas DR, al-Abbadi M, Tabaczka P, et al. c-Kit expression in desmoids fibromatosis. Comparative immunohistochemical evaluation of two commercial antibodies[J]. Am J Clin Pathol, 2003, 119(3): 339-345.
15. 　黄恺,傅红. 韧带样瘤的诊治进展及热点问题[J]. 中国癌症杂志, 2010, 20(3): 227-231.
16. 　黄恺, 王春萌, 师英强, 等. 151例韧带样瘤的疗效及预后分析[J].中国癌症杂志, 2011, 21(1): 61-66.
17. 　Gronchi A, Casali PG, Mariani L, et al. Quality of surgery and outcome in extra-abdominal aggressive fibromatosis: a series of patients surgically treated at a single institution[J]. J Clin Oncol, 2003, 21(7): 1390-1397.
18. 　Bonvalot S, Eldweny H, Haddad V, et al. Extra-abdominal primary fibromatosis: aggressive management could be avoided in a subgroup of patients [J]. EJSO, 2008, 34(4): 462-468.
19. 　陈懿,马洪良.手术联合放疗治疗腹壁外侵袭性纤维瘤病[J].中国现代医学杂志, 2009, 4(19): 631.

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韧带样型纤维瘤病的诊治进展

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