Diagnosis and Management for a Case of Primary Liver Perivascular Epitheliod Cell Tumor and Literatures Review_CHINESE JOURNAL OF BASES AND CLINICS IN GENERAL SURGERY

Authors：

 吴全 ¹ , 赵景明 ¹ ,  郭晏同 ¹ , 徐奇奇 ¹ , 付强 ¹ , 刘宝岳 ²

1. ;
2. ;

Corresponding author：

郭晏同, Email: guoyantong@aliyun.com

Keywords：

肝脏; 血管周上皮样细胞肿瘤

DOI：

10.7507/1007-9424.20140313

Video：

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Abstract Full text Figures/Tables Video References Cited by

目的结合近期收治的1例肝脏血管周上皮样细胞肿瘤（perivascular epitheliod cell tumor，PEComa）的病例特点，总结该疾病的诊治体会。方法回顾分析2013年9月笔者所在医院成功收治的1例肝脏原发PEComa的诊治过程，并结合既往文献报道，总结和复习该疾病的临床特点以及处理方法。结果肝脏PEComa较为罕见，起病隐匿，症状缺乏特异性，临床诊断困难，多依赖病理学检查证实，手术切除是有效的治疗手段。结论提高本病影像学特征的认识有助于术前肿瘤性质的判断，本病预后较好，但术后仍需要长期密切观察随访。

Citation： 吴全, 赵景明, 郭晏同, 徐奇奇, 付强, 刘宝岳. Diagnosis and Management for a Case of Primary Liver Perivascular Epitheliod Cell Tumor and Literatures Review. CHINESE JOURNAL OF BASES AND CLINICS IN GENERAL SURGERY, 2014, 21(10): 1302-1304. doi: 10.7507/1007-9424.20140313 Copy

1.	Martignoni G, Pea M, Reghellin D, et al. PEComas:the past, the present and the future[J]. Virchows Arch, 2008, 452(2):119-132.
2.	Yang X, Li A, Wu M. Hepatic angiomyolipoma:clinical, imaging and pathological features in 178 cases[J]. Med Oncol, 2013, 30(1):416.
3.	Zhao LJ, Yang YJ, Wu H, et al. Perivascular epithelioid cell tumor of the liver:a case report and literature review[J]. Eur Rev Med Pharmacol Sci, 2013, 17(12):1665-1668.
4.	Selvaggi F, Risio D, Claudi R, et al. Malignant PEComa:a case report with emphasis on clinical and morphological criteria[J]. BMC Surg, 2011, 11:3.
5.	Folpe AL, Kwiatkowski DJ. Perivascular epithelioid cell neopl-asms:pathology and pathogenesis[J]. Hum Pathol, 2010, 41(1):1-15.
6.	Ji JS, Lu CY, Wang ZF, et al. Epithelioid angiomyolipoma of the liver:CT and MRI features[J]. Abdom Imaging, 2013, 38(2):309-314.
7.	Rosado E, Cabral P, Campo M, et al. Mesenchymal hamartoma of the liver-a case report and literature review[J]. J Radiol Case Rep, 2013, 7(5):35-43.
8.	Lee SJ, Kim SY, Kim KW, et al. Hepatic angiomyolipoma with minimal fat, mimicking hepatocellular carcinoma[J]. Clin Mol Hepatol, 2012, 18(3):330-335.
9.	Saito Y, Shimada M, Utsunomiya T, et al. Hepatic epithelioid angiomyolipoma with arterioportal venous shunting mimicking hepatocellular carcinoma:report of a case[J]. J Med Invest, 2013, 60(3-4):262-266.
10.	Yang CY, Ho MC, Jeng YM, et al. Management of hepatic ang-iomyolipoma[J]. J Gastrointest Surg, 2007, 11(4):452-457.
11.	Vagefi PA, Eilers H, Hiniker A, et al. Liver transplantation for giant hepatic angiomyolipoma[J]. Liver Transpl, 2011, 17(8):985-986.
12.	郑树国, 田驹.腹腔镜肝切除术适应证再探讨[J].中国普外基础与临床杂志, 2013, 20(4):352-355.
13.	Peng J, Yu B, Wang J, et al. An unresectable malignant perivascular epithelioid cell tumor resistant to multiple combined chemotherapies:a unique case report[J]. J Pediatr Hematol Oncol, 2010, 32(4):136-138.
14.	Chang Z, Zhang JM, Ying JQ, et al. Characteristics and treatment strategy of hepatic angiomyolipoma:a series of 94 patients collected from four institutions[J]. J Gastrointestin Liver Dis, 2011, 20(1):65-69.
15.	Zhou YM, Li B, Xu F, et al. Clinical features of hepatic angiom-yolipoma[J]. Hepatobiliary Pancreat Dis Int, 2008, 7(3):284-287.
16.	Jafari A, Fischer HP, Von Websky M, et al. Primary perivascular epitheloid cell tumour (PEComa) of the liver:case report and review of the literature[J]. Z Gastroenterol, 2013, 51(9):1096-1100.

1. Martignoni G, Pea M, Reghellin D, et al. PEComas:the past, the present and the future[J]. Virchows Arch, 2008, 452(2):119-132.
2. Yang X, Li A, Wu M. Hepatic angiomyolipoma:clinical, imaging and pathological features in 178 cases[J]. Med Oncol, 2013, 30(1):416.
3. Zhao LJ, Yang YJ, Wu H, et al. Perivascular epithelioid cell tumor of the liver:a case report and literature review[J]. Eur Rev Med Pharmacol Sci, 2013, 17(12):1665-1668.
4. Selvaggi F, Risio D, Claudi R, et al. Malignant PEComa:a case report with emphasis on clinical and morphological criteria[J]. BMC Surg, 2011, 11:3.
5. Folpe AL, Kwiatkowski DJ. Perivascular epithelioid cell neopl-asms:pathology and pathogenesis[J]. Hum Pathol, 2010, 41(1):1-15.
6. Ji JS, Lu CY, Wang ZF, et al. Epithelioid angiomyolipoma of the liver:CT and MRI features[J]. Abdom Imaging, 2013, 38(2):309-314.
7. Rosado E, Cabral P, Campo M, et al. Mesenchymal hamartoma of the liver-a case report and literature review[J]. J Radiol Case Rep, 2013, 7(5):35-43.
8. Lee SJ, Kim SY, Kim KW, et al. Hepatic angiomyolipoma with minimal fat, mimicking hepatocellular carcinoma[J]. Clin Mol Hepatol, 2012, 18(3):330-335.
9. Saito Y, Shimada M, Utsunomiya T, et al. Hepatic epithelioid angiomyolipoma with arterioportal venous shunting mimicking hepatocellular carcinoma:report of a case[J]. J Med Invest, 2013, 60(3-4):262-266.
10. Yang CY, Ho MC, Jeng YM, et al. Management of hepatic ang-iomyolipoma[J]. J Gastrointest Surg, 2007, 11(4):452-457.
11. Vagefi PA, Eilers H, Hiniker A, et al. Liver transplantation for giant hepatic angiomyolipoma[J]. Liver Transpl, 2011, 17(8):985-986.
12. 郑树国, 田驹.腹腔镜肝切除术适应证再探讨[J].中国普外基础与临床杂志, 2013, 20(4):352-355.
13. Peng J, Yu B, Wang J, et al. An unresectable malignant perivascular epithelioid cell tumor resistant to multiple combined chemotherapies:a unique case report[J]. J Pediatr Hematol Oncol, 2010, 32(4):136-138.
14. Chang Z, Zhang JM, Ying JQ, et al. Characteristics and treatment strategy of hepatic angiomyolipoma:a series of 94 patients collected from four institutions[J]. J Gastrointestin Liver Dis, 2011, 20(1):65-69.
15. Zhou YM, Li B, Xu F, et al. Clinical features of hepatic angiom-yolipoma[J]. Hepatobiliary Pancreat Dis Int, 2008, 7(3):284-287.
16. Jafari A, Fischer HP, Von Websky M, et al. Primary perivascular epitheloid cell tumour (PEComa) of the liver:case report and review of the literature[J]. Z Gastroenterol, 2013, 51(9):1096-1100.

CHINESE JOURNAL OF BASES AND CLINICS IN GENERAL SURGERY

Diagnosis and Management for a Case of Primary Liver Perivascular Epitheliod Cell Tumor and Literatures Review

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