目的:通过分析平山病的磁共振成像(MRI)表现特点和结合文献复习,提高其诊断水平。方法:报道1例经临床证实的平山病患者的MRI表现,并复习文献,探讨MRI表现的相关发病机制及病理解剖基础。结果:采用西门子Sonata 1.5T磁共振机,先取生理状态下颈椎MRI检查,显示脊髓前角非对称性萎缩和脊髓背侧硬膜外静脉丛扩张;再行屈颈状态下MRI检查,可见颈髓的硬脊膜后壁向前推移,下段颈髓局限受压变细征。结论:平山病有特征性MRI表现,结合临床、常规位和功能位屈颈状态的MRI检查,可以提示平山病。
Citation:
YI Xuebing,DENG Kaihong,ZHANG Dezhou. The Hirayama Disease’s MRI Features and Literature Review. West China Medical Journal, 2009, 24(1): 150-152. doi:
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Robberecht W,Aguirre T,Van den Bosch L,et al.Familial juvenile focal amyotrophy of the upper extremity (Hirayama Disease).Superoxide dismutase 1 genotype and activity[J].Arch Neurol,1997,54(1):46-50..
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Hirayama K,Tokumamu Y.Cervical dural sac and spinal cord in juvenile muscular atrophy of distal upper extremity[J].Neurology,2000,54(10):1922-1926..
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Chen CJ,Chen CM,Wu CL,et al.Hirayama Disease:MR Diagnosis[J].AJN R Am J Neuroradiol,1998,19(2):365-384..
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Bland JH.Basic anatomy[M].2nd ed.Philadelphia,Pa:Saunders,1994:41-70..
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Toma S,Shiozawa Z.Amyotrophic cervical myelopathy in adolescence[J].J Neurol Neurosurg Psychiatry,1995,58 (1):56-64.
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- 1. Robberecht W,Aguirre T,Van den Bosch L,et al.Familial juvenile focal amyotrophy of the upper extremity (Hirayama Disease).Superoxide dismutase 1 genotype and activity[J].Arch Neurol,1997,54(1):46-50..
- 2. Schroder R,Keller E,Flacke S,et al.MRI findings in Hirayama’s disease:flexioninduced cervical myelopathy or intrinsic motor neuron disease?[J]J Neurol,1999,246(11):10691074..
- 3. Hirayama K,Tokumamu Y.Cervical dural sac and spinal cord in juvenile muscular atrophy of distal upper extremity[J].Neurology,2000,54(10):1922-1926..
- 4. Chen CJ,Chen CM,Wu CL,et al.Hirayama Disease:MR Diagnosis[J].AJN R Am J Neuroradiol,1998,19(2):365-384..
- 5. Bland JH.Basic anatomy[M].2nd ed.Philadelphia,Pa:Saunders,1994:41-70..
- 6. Toma S,Shiozawa Z.Amyotrophic cervical myelopathy in adolescence[J].J Neurol Neurosurg Psychiatry,1995,58 (1):56-64.