Idiopathic cranial hypertension (IIH) is a neurological disorder that causes an unexplained increase in intracranial pressure. Its symptoms are chronic headache and visual impairment with typical unilateral or bilateral disk edema. The diagnostic procedure is mainly based on the exclusion of diagnostic thinking, which requires the imaging examination of the whole body and nervous system. Current treatment strategies for IIH include a combination of weight loss, medication, and surgery to reduce intracranial pressure and relieve associated symptoms, maximize visual function preservation, and improve prognosis. In the future, it is necessary to further improve the diagnostic process and criteria of IIH, guide personalized treatment and prognosis judgment, and effectively use artificial intelligence segmentation and combined imaging omics technology to improve the intelligent diagnosis rate of the disease.