ObjectiveTo summarize the research progress of one-stage posterior hemivertebra resection for congenital kyphoscoliosis. MethodsThe domestic and foreign related literature about spinal hemivertebra deformity,and many aspects of its operation mode,operation timing,the fixed segment,and operation complications were summarized and analysed. ResultsThe hemivertebra resection can remove teratogenic factors directly,and is favor by the majority of domestic and foreign physicians,but the procedure,indications,long-term effectiveness,and postoperative complications are still unconcern,and the operation timing and fixed-fused segment is still controversial. ConclusionThe operation timing and the fixed segment of one-stage posterior hemivertebra resection for congenital kyphoscoliosis need further research.