Case analysis：Imaging manifestations of fibropolycystic liver diseases_CHINESE JOURNAL OF BASES AND CLINICS IN GENERAL SURGERY

Authors：

WANG Yuanyuan , LUO Chunyan , CHEN Weixia ,  QIN Yun

Department of Radiology, West China Hospital, Sichuan University, Chengdu 610041, P. R. China;

Corresponding author：

QIN Yun, Email: qinyun@wchscu.cn

Keywords：

fibropolycystic liver diseases; bile duct hamartoma; congenital hepatic fibrosis; Caroli’s disease; imaging manifestation

DOI：

10.7507/1007-9424.202402024

Video：

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Abstract Full text Figures/Tables Video References Cited by

Fibropolycystic liver diseases (FLDs) is a rare genetic disorder, including bile duct hamartomas, congenital hepatic fibrosis, polycystic liver disease, Caroli’s disease, and choledochal cysts. Fibropolycystic liver diseases has received little clinical attention and exhibits a variety of imaging manifestations, leading to a high likelihood of missed diagnosis and misdiagnosis. Through this case, we delineate the characteristic imaging manifestations of the disease and its underlying pathological mechanisms. Our objective is to enhance readers' comprehension of the disease and thereby reduce the rate of missed diagnosis and misdiagnosis of the disease.

Citation： WANG Yuanyuan, LUO Chunyan, CHEN Weixia, QIN Yun. Case analysis：Imaging manifestations of fibropolycystic liver diseases. CHINESE JOURNAL OF BASES AND CLINICS IN GENERAL SURGERY, 2024, 31(9): 1059-1062. doi: 10.7507/1007-9424.202402024 Copy

1.	Sharbidre K, Zahid M, Venkatesh SK, et al. Imaging of fibropolycystic liver disease. Abdom Radiol (NY), 2022, 47(7): 2356-2370.
2.	Mortelé KJ, Ros PR. Cystic focal liver lesions in the adult: differential CT and MR imaging features. Radiographics, 2001, 21(4): 895-910.
3.	Brancatelli G, Federle MP, Vilgrain V, et al. Fibropolycystic liver disease: CT and MR imaging findings. Radiographics, 2005, 25(3): 659-670.
4.	Yacoub JH, Clark JA, Paal EE, et al. Approach to cystic lesions in the abdomen and pelvis, with radiologic-pathologic correlation. Radiographics, 2021, 41(5): 1368-1386.
5.	朱艳艳, 孙英姿, 杨丽, 等. 肝内胆管错构瘤的影像学诊断. 医学影像学杂志, 2020, 30(12): 2254-2257.
6.	Shorbagi A, Bayraktar Y. Experience of a single center with congenital hepatic fibrosis: a review of the literature. World J Gastroenterol, 2010, 16(6): 683-690.
7.	Alsomali MI, Yearsley MM, Levin DM, et al. Diagnosis of congenital hepatic fibrosis in adulthood. Am J Clin Pathol, 2020, 153(1): 119-125.
8.	Akhan O, Karaosmanoğlu AD, Ergen B. Imaging findings in congenital hepatic fibrosis. Eur J Radiol, 2007, 61(1): 18-24.
9.	Zeitoun D, Brancatelli G, Colombat M, et al. Congenital hepatic fibrosis: CT findings in 18 adults. Radiology, 2004, 231(1): 109-116.
10.	李菲菲, 傅兆庆, 任万华. 先天性肝纤维化伴Caroli病一例. 中华肝脏病杂志, 2019, 27(6): 463-465.
11.	Mamone G, Carollo V, Cortis K, et al. Magnetic resonance imaging of fibropolycystic liver disease: the spectrum of ductal plate malformations. Abdom Radiol (NY), 2019, 44(6): 2156-2171.
12.	钟金晶, 严律南, 王文涛, 等. 先天性肝纤维化合并Caroli综合征1例报道. 中国普外基础与临床杂志, 2012, 19(8): 916.
13.	张一博, 李新华. 先天性肝纤维化现状和研究进展. 临床内科杂志, 2024, 41(4): 245-248.
14.	Zhang ZY, Wang ZM, Huang Y. Polycystic liver disease: Classification, diagnosis, treatment process, and clinical management. World J Hepatol, 2020, 12(3): 72-83.
15.	康宇航, 周永杰, 严律南, 等. 多囊性肝病的诊断治疗进展. 中国普外基础与临床杂志, 2022, 29(10): 1368-1375.
16.	Zhong Y, Peng S, Yang Y. Hepatobiliary and pancreatic: caroli syndrome: egg-like sign on CT. J Gastroenterol Hepatol, 2020, 35(2): 180. doi: 10.1111/jgh.14822.
17.	肖玉妹, 彭婷婷, 刘映霞. 病理证实的症状、影像不典型的Caroli病1例. 中华肝脏病杂志, 2021, 29(2): 172-174.

1. Sharbidre K, Zahid M, Venkatesh SK, et al. Imaging of fibropolycystic liver disease. Abdom Radiol (NY), 2022, 47(7): 2356-2370.
2. Mortelé KJ, Ros PR. Cystic focal liver lesions in the adult: differential CT and MR imaging features. Radiographics, 2001, 21(4): 895-910.
3. Brancatelli G, Federle MP, Vilgrain V, et al. Fibropolycystic liver disease: CT and MR imaging findings. Radiographics, 2005, 25(3): 659-670.
4. Yacoub JH, Clark JA, Paal EE, et al. Approach to cystic lesions in the abdomen and pelvis, with radiologic-pathologic correlation. Radiographics, 2021, 41(5): 1368-1386.
5. 朱艳艳, 孙英姿, 杨丽, 等. 肝内胆管错构瘤的影像学诊断. 医学影像学杂志, 2020, 30(12): 2254-2257.
6. Shorbagi A, Bayraktar Y. Experience of a single center with congenital hepatic fibrosis: a review of the literature. World J Gastroenterol, 2010, 16(6): 683-690.
7. Alsomali MI, Yearsley MM, Levin DM, et al. Diagnosis of congenital hepatic fibrosis in adulthood. Am J Clin Pathol, 2020, 153(1): 119-125.
8. Akhan O, Karaosmanoğlu AD, Ergen B. Imaging findings in congenital hepatic fibrosis. Eur J Radiol, 2007, 61(1): 18-24.
9. Zeitoun D, Brancatelli G, Colombat M, et al. Congenital hepatic fibrosis: CT findings in 18 adults. Radiology, 2004, 231(1): 109-116.
10. 李菲菲, 傅兆庆, 任万华. 先天性肝纤维化伴Caroli病一例. 中华肝脏病杂志, 2019, 27(6): 463-465.
11. Mamone G, Carollo V, Cortis K, et al. Magnetic resonance imaging of fibropolycystic liver disease: the spectrum of ductal plate malformations. Abdom Radiol (NY), 2019, 44(6): 2156-2171.
12. 钟金晶, 严律南, 王文涛, 等. 先天性肝纤维化合并Caroli综合征1例报道. 中国普外基础与临床杂志, 2012, 19(8): 916.
13. 张一博, 李新华. 先天性肝纤维化现状和研究进展. 临床内科杂志, 2024, 41(4): 245-248.
14. Zhang ZY, Wang ZM, Huang Y. Polycystic liver disease: Classification, diagnosis, treatment process, and clinical management. World J Hepatol, 2020, 12(3): 72-83.
15. 康宇航, 周永杰, 严律南, 等. 多囊性肝病的诊断治疗进展. 中国普外基础与临床杂志, 2022, 29(10): 1368-1375.
16. Zhong Y, Peng S, Yang Y. Hepatobiliary and pancreatic: caroli syndrome: egg-like sign on CT. J Gastroenterol Hepatol, 2020, 35(2): 180. doi: 10.1111/jgh.14822.
17. 肖玉妹, 彭婷婷, 刘映霞. 病理证实的症状、影像不典型的Caroli病1例. 中华肝脏病杂志, 2021, 29(2): 172-174.

CHINESE JOURNAL OF BASES AND CLINICS IN GENERAL SURGERY

Case analysis：Imaging manifestations of fibropolycystic liver diseases

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